Biellik 2 y C. Clements 3. Fuera del domicilio, los sitios de mayor riesgo son los centros educacionales, estadios deportivos, instituciones religiosas, orfelinatos, campamentos para refugiados y servicios de salud 4 , 5. El virus se excreta en la nasofaringe de personas enfermas y se expele en gotitas suspendidas en el aire al toser.

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Systemic mastocytosis in childhood: report of 3 cases. Fernandes 1 , Beatriz C. Cestari 5. Objective: mastocytosis comprises a group of diseases characterized by accumulation of mast cells on the skin, with the possibility of affecting other systems.

Symptoms can be exclusively cutaneous, associated with symptoms of the organs involved or even systemic, due to the release of chemical mediators.

Three cases of systemic mastocytosis are described, each case presenting different manifestations of the disorder. Description: the first report is about a patient with urticaria pigmentosa that presented persistent lesions until puberty when systemic manifestations initiated with lymphoreticular involvement, splenomegaly and bone marrow infiltration.

In the second case, the child had bullous mastocytosis associated with gastrointestinal symptoms, whose investigation showed mast cell infiltration in the intestinal wall. The third patient presented an early and extensive cutaneous manifestation of mastocytosis, with a dramatic evolution to shock and posterior death. Discussion: clinical aspects, treatment and prognosis of such forms of the disease are discussed.

Havia feito diversos tratamentos para parasitoses intestinais e piodermites. A ecografia abdominal confirmou a hepatoesplenomegalia. Estudio de casos. Actas Dermosifiliogr ; Greaves MW. Textbook of Dermatology. Oxford: Blackwell Science; Metcalfe DD. The mastocytosis syndrome. Dermatology in general medicine.

Austen: Mc Graw Hill; The mast cell and mast cell disease. J Am Acad Dermatol ; Mastocytosis with skin manifestations: current status. J Eur Acad Dermatol Venereol ; Pediatric mastocytosis. J Invest Dermatol ;SS. Classification and diagnosis of mastocytosis: current status. J Invest Dermatol ;S-4S. Textbook of Pediatric Dermatology. Mastocytosis and the mast cell. Systemic mast cell disease: analysis of 58 cases and literature review. Medicine ; Stein DH. Mastocytosis: a review.

Pediatric Dermatol ; Tharp MD. Mast cell disease and its diagnosis. J Invest Dermatol ; 6 Setcalfe DD. Bullous mastocytosis: a fatal outcome. Systemic mastocytosis: retrospective review of a decade's clinical experience at the Brigham and Women's Hospital. Blood findings in generalized mastocytosis: evidence of frequent simultaneous occurrence of myeloproliferative disorders.

Br J Hematol ; Urticaria pigmentosa associated with Wilms tumor. Pediatr Dermatol ; Bullous urticaria pigmentosa. Cutis ; Interferon-a in combination with corticosteroids improves systemic mast cell disease. Br J Dermatol ; Tania F. Cestari Fax: 51 Artigo submetido em All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

Services on Demand Journal. Carlos Gomes, cj. How to cite this article.


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